Search on: HEMOPHAGOCYTIC SYNDROMES 
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Descriptor English:   Lymphohistiocytosis, Hemophagocytic 
Descriptor Spanish:   Linfohistiocitosis Hemofagocítica 
Descriptor Portuguese:   Linfo-Histiocitose Hemofagocítica 
Synonyms English:   Erythrophagocytic Lymphohistiocytoses, Familial
Erythrophagocytic Lymphohistiocytosis, Familial
Familial Erythrophagocytic Lymphohistiocytoses
Familial Erythrophagocytic Lymphohistiocytosis
Familial Hemophagocytic Histiocytoses
Familial Hemophagocytic Histiocytosis
Familial Hemophagocytic Lymphocytoses
Familial Hemophagocytic Lymphocytosis
Familial Hemophagocytic Lymphohistiocytoses
Familial Hemophagocytic Lymphohistiocytosis
Familial Hemophagocytic Reticuloses
Familial Hemophagocytic Reticulosis
Familial Histiocytic Reticuloses
Familial Histiocytic Reticulosis
Hemophagocytic Histiocytoses, Familial
Hemophagocytic Histiocytosis, Familial
Hemophagocytic Hymphohistiocytoses, Primary
Hemophagocytic Hymphohistiocytosis, Primary
Hemophagocytic Lymphocytoses, Familial
Hemophagocytic Lymphocytosis, Familial
Hemophagocytic Lymphohistiocytoses
Hemophagocytic Lymphohistiocytoses, Familial
Hemophagocytic Lymphohistiocytoses, Primary
Hemophagocytic Lymphohistiocytosis
Hemophagocytic Lymphohistiocytosis Familial -1
Hemophagocytic Lymphohistiocytosis Familial 1
Hemophagocytic Lymphohistiocytosis, Familial
Hemophagocytic Lymphohistiocytosis, Familial, 1
Hemophagocytic Lymphohistiocytosis, Primary
Hemophagocytic Reticuloses, Familial
Hemophagocytic Reticulosis, Familial
Hemophagocytic Syndrome
Hemophagocytic Syndrome, Infection Associated
Hemophagocytic Syndrome, Infection-Associated
Hemophagocytic Syndrome, Reactive
Hemophagocytic Syndromes
Histiocytic Reticuloses, Familial
Histiocytic Reticulosis, Familial
Histiocytoses, Familial Hemophagocytic
Histiocytosis, Familial Hemophagocytic
Hymphohistiocytoses, Primary Hemophagocytic
Hymphohistiocytosis, Primary Hemophagocytic
Infection-Associated Hemophagocytic Syndrome
Lymphocytoses, Familial Hemophagocytic
Lymphocytosis, Familial Hemophagocytic
Lymphohistiocytoses, Familial Erythrophagocytic
Lymphohistiocytoses, Familial Hemophagocytic
Lymphohistiocytoses, Hemophagocytic
Lymphohistiocytoses, Primary Hemophagocytic
Lymphohistiocytosis, Familial Erythrophagocytic
Lymphohistiocytosis, Familial Hemophagocytic
Lymphohistiocytosis, Primary Hemophagocytic
Primary Hemophagocytic Hymphohistiocytoses
Primary Hemophagocytic Hymphohistiocytosis
Primary Hemophagocytic Lymphohistiocytoses
Primary Hemophagocytic Lymphohistiocytosis
Reactive Hemophagocytic Syndrome
Reticuloses, Familial Hemophagocytic
Reticuloses, Familial Histiocytic
Reticulosis, Familial Hemophagocytic
Reticulosis, Familial Histiocytic  
Tree Number:   C15.604.250.410.575
Definition English:   A group of related disorders characterized by LYMPHOCYTOSIS; HISTIOCYTOSIS; and hemophagocytosis. The two major forms are familial and reactive. 
History Note English:   2006; use HISTIOCYTOSIS, NON-LANGERHANS CELL 1990-2005 
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications CN congenital
DI diagnosis DG diagnostic imaging
DH diet therapy DT drug therapy
EC economics EM embryology
EN enzymology EP epidemiology
EH ethnology ET etiology
GE genetics HI history
IM immunology ME metabolism
MI microbiology MO mortality
NU nursing PS parasitology
PA pathology PP physiopathology
PC prevention & control PX psychology
RT radiotherapy RH rehabilitation
SU surgery TH therapy
UR urine VE veterinary
VI virology  
Record Number:   50506 
Unique Identifier:   D051359 

Occurrence in VHL:
 

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